Giant multinodular infantile fibrosarcoma: a case report

Authors

  • Aliyu M. Usman Department of Radiotherapy and Oncology, Usmanu Danfodiyo University Teaching Hospital, Sokoto, Nigeria
  • Okuofo C. Ehiosa Department of Radiotherapy and Oncology, Usmanu Danfodiyo University Teaching Hospital, Sokoto, Nigeria
  • Okwonna O. Charles Department of Radiotherapy and Oncology, Usmanu Danfodiyo University Teaching Hospital, Sokoto, Nigeria
  • Abdullahi Adamu Department of Radiotherapy and Oncology, Ahmadu Bello University Teaching Hospital, Zaria- Shika, Kaduna State, Nigeria

DOI:

https://doi.org/10.18203/2320-6012.ijrms20180324

Keywords:

Chemotherapy, Fibrosarcoma, Giant, Infantile, Radiotherapy

Abstract

Infantile fibrosarcoma is a rare type of soft tissue sarcoma seen in children usually less than 2years of age. Few cases of giant infantile fibrosarcoma have been reported in literature. We report a rare case of a giant multi-nodular infantile fibrosarcoma in the left anterolateral chest wall in a 7-year-old boy. The tumour was said to have been recurrent twice for about 6 years. At presentation patient was evaluated and was commenced on 6 cycles of neoadjuvant chemotherapy with vincristine, adriamycin and cyclophosphamide (VAC) regimen to alternate with Ifosfamide/Etoposide (IE) regimen with very good response. Thereafter, had a wide local excision of the tumour and then had 4 more cycles of adjuvant chemotherapy. His 6months follow up showed no evidence of tumour recurrence. Infantile fibrosarcoma is said to be chemo-sensitive tumour with very good response, though surgical excision is the main treatment of choice and overall it is said to have a good prognosis.

Author Biography

Okwonna O. Charles, Department of Radiotherapy and Oncology, Usmanu Danfodiyo University Teaching Hospital, Sokoto, Nigeria

Senior registrar, department of radiotherapy and oncology, UDUTH

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Published

2018-01-24

How to Cite

Usman, A. M., Ehiosa, O. C., Charles, O. O., & Adamu, A. (2018). Giant multinodular infantile fibrosarcoma: a case report. International Journal of Research in Medical Sciences, 6(2), 701–703. https://doi.org/10.18203/2320-6012.ijrms20180324

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Section

Case Reports