Parachute mitral valve with late presentation: rare case reports
DOI:
https://doi.org/10.18203/2320-6012.ijrms20182935Keywords:
Congenital mitral stenosis, Parachute mitral valve, Shone’s complexAbstract
Congenital mitral stenosis involves the annulus, the zone immediately above and contiguous with the annulus, the leaflets, the chordae tendineae, and the papillary muscles. In a parachute mitral valve (PMV), all chordae tendineae which are usually shorter and thicker than normal type, inserted into this single papillary muscle. This condition restricts the motion of leaflets and obstructs the blood flow into the left ventricle during diastole. Here we present two cases of severe congenital mitral stenosis with severe pulmonary hypertension due to parachute mitral valve that allowed survival into adulthood without any specific treatment.
References
Silbiger JJ, Bazaz R. Contemporary insights into the functional anatomy of the mitral valve. Am Heart J. 2009;158(6):887-95.
Shone JD, Sellers RD, Anderson RC, Adams P, Lillehei CW, Edwards JE. The developmental complex of parachute mitral valve, supra valvular ring of left atrium, subaortic stenosis, and coarctation of aorta. Am J Cardiolo. 1963;11(6):714-25.
Godoy I, Tantibhedhyangkul W, Karp R, Lang R. Images in cardiovascular medicine. Cor triatriatum. Circulation. 1998;98:2781.
Collins-Nakai RL, Rosenthal A, Castaneda AR, Bernhard WF, Nadas AS. Congenital mitral stenosis. A review of 20 years’ experience. Circulation. 1977;56:1039-47.
Tandon R, Moller JH, Edwards JE. Anomalies associated with the parachute mitral valve: a pathologic analysis of 52 cases. Can J Cardiol. 1986;2:278-81.
Smallhorn J, Tommasini G, Deanfield J, Douglas J, Gibson D, Macartney F. Congenital mitral stenosis. Anatomical and functional assessment by echocardiography. Br Heart J. 1981;45:527-34.
Hakim FA, Kendall CB, Alharthi M, Mancina JC, Tajik JA, Mookadam F. Parachute mitral valve in adults: a systematic overview. Echocardiography 2010;27(5):581-6.
Toufan M, Mahmoudi SS. Isolated parachute mitral valve in a 29 years old female; a case report. J Cardiovasc Thorac Res. 2016;8(1):43-5.
Ruckman RN, Van Praagh R. Anatomic types of congenital mitral stenosis: report of 49 autopsy cases with consideration of diagnosis and surgical implications. Am J Cardiol. 1978;42:592-601.
Marino BS, Kruge LE, Cho CJ, Tomlinson RS, Shera D, Weinberg PM, et al. Parachute mitral valve: morphologic descriptors, associated lesions, and outcomes after biventricular repair. J Thorac Cardiovasc Surg. 2009;137(2):385-93.