DOI: https://dx.doi.org/10.18203/2320-6012.ijrms20222873
Published: 2022-10-28

Hepatic undifferentiated embryonal sarcoma as a cause of acute abdomen

Karina Sánchez-Reyes, Marco P. Tovar-Ferrer, Erik D. Álvarez-Sores, Javier Cerrillo-Ávila, Estrella Aguilar-Hernández, Rocio L. Arreola-Rosales, Tania Gamboa-Jiménez, José L. Martínez Ordaz

Abstract


Primary liver sarcoma represents less than 1% of all primary liver tumors. Hepatic undifferentiated embryonal sarcoma (HUES) is included in the histologic group of primary liver sarcomas. HUES is a rare malignant liver tumor with a low incidence in the adult population. At moment there is no tumor marker that increases suspicion or diagnosis Early diagnosis is key to rise the possibilities of long-term survival. It has currently improved its prognosis through multidisciplinary management with surgical resection and chemotherapy. This case report presents a 20-year-old female patient with acute abdomen and anemic syndrome secondary to spontaneous rupture of a HUES requiring medical management initially based on resuscitation and arterial embolization with subsequent surgical resection.


Keywords


HUES, Hepatic bisegmentectomy, Hepato-splenicscintigraphy

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