Myxoid liposarcoma presenting like a cystic neck swelling
Keywords:
Myxoid, Liposarcoma, Cystic swelling, Sarcoma, Neck swellingAbstract
Soft tissue sarcomas are rare and unusual neoplasm’s, accounting for approximately 1% of adult human cancers and 15% of pediatric malignancies. Most liposarcomas occur in deep soft tissues of the extremities and retroperitoneum; only a very small percentage (as low as 2%) occurs in the head and neck. Here we present a case of a 48yr old male with a painless mass in the neck clinically presenting as a cystic swelling. The CT neck was suggestive of cystic lesion in the neck representing benign cystic lesion. The swelling was excised and sent for histopathology which was suggestive of myxoid liposarcoma. The patient was planned for wide excision of the edges and scar and adjuvant chemo and radio therapy.
References
Patel SG, Shaha AR, Shah JP. Soft tissue sarcomas of the head and neck: an update. Am J Otolaryngol. 2001;22:2-18.
Pandey M, Chandramohan K, Thomas G, Mathew A, Sebastian P, Somanathan T, Abrham EK, et al. Soft tissue sarcoma of the head and neck in adults. Int J Oral Maxillofac Surg. 2003;32:43-8.
Colville RJ, Charlton F, Kelly CG, Nicoll JJ, McLean NR. Multidisciplinary management of head and neck sarcomas. Head Neck. 2005;27:814-24.
Spillane AJ, Fisher C, Thomas JM. Myxoid liposarcoma: the frequency and the natural history of nonpulmonary soft tissue metastases. Ann Surg Oncol. 1999;6:389-94.
Courtney M. Townsend, R. Daniel Beauchamp, B. Mark Evers, Kenneth L. Mattox. Soft tissue sarcomas. In: Samuel Singer, eds. Sabiston Text Book of Surgery. 19th ed. Philadelphia: Saunders; 2012.
Loubignac F, Bourtoul C, Chapel F. Myxoid liposarcoma: a rare soft-tissue tumor with a misleading benign appearance. World J Surg Oncol. 2009;7:42.
Dujardin F, Debled M, Guillemet C, Simonet J, Hamidou H, Cambon- Michot C, et al. Prise en charge des tumeurs desparties molles de l'appareil locomoteur de l'adulte. Rev Chir Orthop. 2006;92:637-50.
Prestwich RJ, Taylor RE, Grimer R. Metastatic myxoid liposarcoma: aggressive multimodality management. Clin Oncol. 2005;17:130-4.
Yang JC, Chang AE, Baker AR, Sindelar WF, Danforth DN, Topalian SL, et al. A randomized prospective study of the benefit of adjuvant radiation therapy in the treatment of soft tissue sarcomas of the extremity. J Clin Oncol. 1998;16:197-203.
