Frontonasal dysplasia- a rare case report

Authors

  • Reena Sharma Department of Obstetrics and Gynaecology, SLBS GMC Mandi at Nerchowk, Himachal Pradesh, India
  • Poojan Dogra Department of Obstetrics and Gynaecology, SLBS GMC Mandi at Nerchowk, Himachal Pradesh, India
  • Kapil Malhotra Department of Obstetrics and Gynaecology, SLBS GMC Mandi at Nerchowk, Himachal Pradesh, India
  • Vivek Kaushal Department of Obstetrics and Gynaecology, Dr. RPGMC Tanda at Kangra, Himachal Pradesh, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20174612

Keywords:

Frontonasal dysplasia, FND, Facial cleft, Neonate

Abstract

Frontonasal dysplasia (FND) is a rare malformative complex affecting the frontal portion of the face, the eyes and the nose; it may occur singly or associated with other clinical signs. We report here a rare case of a full-term male baby who presented with features of FND. There was no history of consanguinity, no positive family history. Antenatal ultrasonography was normal. Though this baby did not survive because the defects were not compatible for the survival. But the developing nations still have handicap in the management of such cases in term of fiancés, surgical correction of such major defects, education and social support in these patients. 

References

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Published

2017-09-28

How to Cite

Sharma, R., Dogra, P., Malhotra, K., & Kaushal, V. (2017). Frontonasal dysplasia- a rare case report. International Journal of Research in Medical Sciences, 5(10), 4640–4642. https://doi.org/10.18203/2320-6012.ijrms20174612

Issue

Section

Case Reports