DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20195025

A case of hereditary sensory and autonomic neuropathy type 4 presenting with chronic trophic ulcers

Kedar M. Tilak, Pratibha B. Shamkuwar

Abstract


Hereditary Sensory and Autonomic Neuropathy (HSAN) is a rare group of diseases involving varying degrees of peripheral nervous system. It is classified into five main types. HSAN type 4 is associated with insensitivity to pain and temperature and anihidrosis. The method of this study was to authors present a case report of a 3 year-old boy with Hereditary Sensory and Autonomic Neuropathy Type 4 presenting with chronic ulcers. Conclusions of this study was to HSAN type IV is a rare condition. There is no definitive treatment available presently for this condition.


Keywords


Anhihidrosis, Hereditary sensory and autonomic neuropathies, pain, Ulcers

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References


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