Anaesthetic management of a patient with non compaction cardiomyopathy for implantable cardioverter defibrillator lead replacement

Authors

  • Kritika Sharma Department of Anaesthesiology and Pain Management, Sir H. N. Reliance Foundation Hospital, Mumbai, Maharashtra, India
  • Deepak Koli Department of Anaesthesiology and Pain Management, Sir H. N. Reliance Foundation Hospital, Mumbai, Maharashtra, India
  • Swati Daftary Department of Anaesthesiology and Pain Management, Sir H. N. Reliance Foundation Hospital, Mumbai, Maharashtra, India
  • Hemant Mehta Department of Anaesthesiology and Pain Management, Sir H. N. Reliance Foundation Hospital, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-6012.ijrms20203471

Keywords:

Arrythmias, Heart failure, Implantable cardioverter defibrillator, Noncompaction cardiomyopathy, Sudden cardiac death

Abstract

Non compaction cardiomyopathy (NCM) is a rare, primary genetically derived cardiomyopathy with a variable clinical presentation ranging from absence of symptoms to congestive heart failure, systemic thromboembolism, arrythmias and sudden cardiac death. Being an uncommon condition, the perioperative concerns in a patient with NCM have not been studied much. With increasing awareness and improved diagnostic tools including high resolution echocardiography and cardiac MRI, there has been an increase in the reporting of cases which stresses on the need for a complete understanding of this form of cardiomyopathy and its perioperative anaesthetic management. Authors report the case of a 24 years old female, with NCM who underwent prophylactic Implantable cardioverter defibrillator (ICD) insertion 5 years ago and was now posted for ICD removal and replacement in view of inappropriate ICD functioning.

References

Frentzou GA, Drinkhill MJ, Turner NA, Ball SG, Ainscough JF. Non-compaction cardiomyopathy. Heart 2013 May 1;99(2):A138.

Oechslin EN, Jost CH, Rojas JR, Kaufmann PA, Jenni R. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000 Aug 1;36(2):493-500.

Rosa LV, Salemi VM, Alexandre LM, Mady C. Noncompaction cardiomyopathy: a current view. Arq Bras Cardiol. 2011 Jul;97(1):e13-9.

Jenni R, Wyss CA, Oechslin EN, Kaurmann PA. Isolated ventricular noncompaction is associated with coronary microcirculatory dysfunction. J Am Coll Cardiol. 2002;39(3):450-4.

Jenni R, Oechslin E, Schneider J, Attenhofer Jost C, Kaufmann PA. Echocardiographic and pathoanatomical characteristics of isolated left ventricular non-compaction: a step towards classification as a distinct cardiomyopathy. Heart. 2001;86(6):666-71.

Petersen SE, Selvanayagam JB, Wiesmann F, Robson MD, Francis JM, Anderson RH, et al. Left ventricular non-compaction: insights from cardiovascular magnetic resonance imaging. J Am College of Cardiol. 2005 Jul 5;46(1):101-5.

Kohli SK, Pantazis AA, Shah JS, Adeyemi B, Jackson G, McKenna WJ, et al. Diagnosis of left-ventricular non-compaction in patients with left-ventricular systolic dysfunction: time for a reappraisal of diagnostic criteria?. Eur Heart J. 2008 Jan 1;29(1):89-95.

Pantazis AA, Elliott PM. Left ventricular noncompaction. Curr Opin Cardiol. 2009;24(3):209-13.

Maron BJ, Towbin JA, Thiene G. Contemporary definitions and classification of the cardiomyopathies. Circulation 2006;113:1807-16.

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Published

2020-07-24

How to Cite

Sharma, K., Koli, D., Daftary, S., & Mehta, H. (2020). Anaesthetic management of a patient with non compaction cardiomyopathy for implantable cardioverter defibrillator lead replacement. International Journal of Research in Medical Sciences, 8(8), 3095–3097. https://doi.org/10.18203/2320-6012.ijrms20203471

Issue

Section

Case Reports