Lhermitte Duclos disease: a rare cerebellar lesion with characteristic neuroimaging features

Authors

  • Pankaj Kant Gupta Department of Neurosurgery, Dr.S N Medical College, Jodhpur, Rajasthan
  • Sunil Garg Department of Neurosurgery, Dr.S N Medical College, Jodhpur, Rajasthan
  • Sharad Thanvi Department of Neurosurgery, Dr.S N Medical College, Jodhpur, Rajasthan

DOI:

https://doi.org/10.18203/2320-6012.ijrms20161836

Keywords:

Lhermitte-Duclos disease/ dysplastic cerebellar gangliocytoma, Hamartomatous, Cowden syndrome

Abstract

Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma) is a rare disorder of uncertain pathogenesis characterized by disarrangement of the normal cerebellar laminar cytoarchitecture. A case of histopathologically confirmed Lhermitte-Duclos disease with characteristic imaging findings and successful surgical management is reported and our findings are discussed.

References

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Published

2017-01-02

How to Cite

Gupta, P. K., Garg, S., & Thanvi, S. (2017). Lhermitte Duclos disease: a rare cerebellar lesion with characteristic neuroimaging features. International Journal of Research in Medical Sciences, 4(6), 2478–2480. https://doi.org/10.18203/2320-6012.ijrms20161836

Issue

Section

Case Reports