DOI: http://dx.doi.org/10.18203/2320-6012.ijrms20161836

Lhermitte Duclos disease: a rare cerebellar lesion with characteristic neuroimaging features

Pankaj Kant Gupta, Sunil Garg, Sharad Thanvi

Abstract


Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma) is a rare disorder of uncertain pathogenesis characterized by disarrangement of the normal cerebellar laminar cytoarchitecture. A case of histopathologically confirmed Lhermitte-Duclos disease with characteristic imaging findings and successful surgical management is reported and our findings are discussed.


Keywords


Lhermitte-Duclos disease/ dysplastic cerebellar gangliocytoma, Hamartomatous, Cowden syndrome

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References


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